Usher Syndrome – Treatment of Usher Syndrome

No cure is found out for Usher Syndrome yet. The best treatment of Usher Syndrome includes early identification of the disorder. This is vital in order to start the educational program the soonest to yield better results. The severity of loss in hearing and vision decides about which treatment should be followed. Even the age and abilities of the patient are considerable factors while deciding the treatment.

Usher Syndrome affects the ability of hearing and vision in a patient. Loss in the ability to hear and retinitis pigmentosa (an eye disease) are the two major symptoms that characterizes the Usher Syndrome. Patients also suffer from some kind of difficulties with balancing due to defective vestibular system. It has three clinical types –

  • type I
  • type II
  • type III

Out of which, type I and type II are most prevalent in the US. They account for about 90-95 % of all cases of children diagnosed with Usher Syndrome.

Hearing aids, cochlear implants, assistive listening devices and other methods of communication like mobility training, orientation or sign languages, Braille instruction, auditory training or low-vision services are involved to cure Usher Syndrome. Some ophthalmologists prefer high dose of vitamin A palmitate to slow the progression of retinitis pigmentosa (RP). But Vitamin A induced cure will not halt the progression. There are a few guidelines available which are noted below –

  • Never substitute vitamin A palmitate with a supplement of beta-carotene.
  • You must not consume more than 15,000 IU which is the recommended dose.
  • You may modify your diet by adding foods with high levels of Vitamin A.
  • If you are considering pregnancy, then you must stop consuming supplements with high dose of Vitamin A. You must not consume them 3 months before your decision to conceive. It can increase the risks of birth defects.

Several factors are considered before deciding which method of treatment must be considered by the physician –

  • age
  • overall condition of the health
  • medical history
  • extent and severity of the disease
  • tolerance towards specific procedures, therapies and medications
  • realistic expectation from the course of therapy
  • preferences

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